Symptomatic thrombosis in Turkish neonates

J Pediatr Hematol Oncol. 2004 Jul;26(7):417-20. doi: 10.1097/00043426-200407000-00003.

Abstract

Objective: To investigate the association of two common prothrombotic mutations, factor V G1691A (FV G1691A) and prothrombin G20210A (PT G20210A), in neonates with thrombosis.

Methods: Twenty-six neonates with thrombosis were assessed with the spectrum of assays for thrombophilia, including the two DNA-based prothrombotic factors.

Results: Eight patients (31%) had the FV G1691A mutation in heterozygous state. PT G20210A mutation was detected in four patients (15%). Overall, two common prothrombotic factors were detected in 12 neonates (46%) and an underlying disease or a triggering event in 18 neonates (69%). Thrombosis was considered to be idiopathic in five neonates (19%).

Conclusions: The pathogenesis of thrombosis in neonates is multi-factorial. Along with underlying diseases or triggering events, congenital prothrombotic factors (FV G1691A and PT G20210A) showed a trend toward a higher frequency in neonates with thrombosis. These data indicate that mutations associated with underlying disorders in neonates may contribute to the development of thromboembolic disease.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Factor V / genetics*
  • Female
  • Genetic Predisposition to Disease
  • Humans
  • Infant, Newborn
  • Male
  • Mutation
  • Prothrombin / genetics*
  • Risk Factors
  • Thrombosis / genetics*
  • Turkey

Substances

  • factor V Leiden
  • Factor V
  • Prothrombin