Treatment of recalcitrant scleromyxedema with thalidomide in 3 patients

J Am Acad Dermatol. 2004 Jul;51(1):126-31. doi: 10.1016/j.jaad.2004.01.058.

Abstract

Scleromyxedema is a generalized, papular, and sclerodermoid form of lichen myxedematosus associated with monoclonal gammopathy and systemic changes. Despite anecdotal reports of success with various agents, no satisfactory treatments are currently available. We report 3 adult patients with recalcitrant scleromyxedema associated with paraproteinemia who were treated with thalidomide. All 3 patients had marked improvement of the skin lesions and joint mobility after the first 2 months of therapy, with further amelioration after 4 months, and reduction in paraprotein levels.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Female
  • Humans
  • Lichenoid Eruptions / complications
  • Lichenoid Eruptions / drug therapy*
  • Male
  • Middle Aged
  • Myxedema / complications
  • Myxedema / drug therapy
  • Paraproteinemias / drug therapy
  • Paraproteinemias / etiology
  • Scleroderma, Systemic / complications
  • Scleroderma, Systemic / drug therapy*
  • Thalidomide / therapeutic use*

Substances

  • Thalidomide