Cell-to-cell contact between normal fibroblasts and lymphoblasts deficient in lysosomal enzymes

Biochim Biophys Acta. 1992 Feb 14;1138(2):143-8. doi: 10.1016/0925-4439(92)90054-q.

Abstract

Human lymphoblasts deficient in iduronate sulfatase or in alpha-N-acetylglucosaminidase acquire discrete levels of enzyme activity after co-culture with human normal skin fibroblasts. This occurs by direct cell-to-cell contact and not by uptake of secreted fibroblast enzyme. The process is dependent on time and on the number of fibroblasts used. Electron-microscopic examination of the co-culture of the two cell types reveals extensive region of intimate contact. Fibroblastic projections appear frequently in close apposition with lymphoblast invaginations; a diffuse micropinocytotic activity is evident only in fibroblastic cells.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Acetylglucosaminidase / deficiency
  • Acetylglucosaminidase / metabolism*
  • Cell Communication*
  • Cell Transformation, Viral
  • Fibroblasts / cytology*
  • Fibroblasts / enzymology
  • Humans
  • Iduronate Sulfatase / metabolism*
  • Lymphocytes / cytology*
  • Lymphocytes / enzymology
  • Microscopy, Electron
  • Mucopolysaccharidoses / enzymology
  • Mucopolysaccharidosis II

Substances

  • Iduronate Sulfatase
  • Acetylglucosaminidase