Fibrillar amyloid-beta peptides kill human primary neurons via NADPH oxidase-mediated activation of neutral sphingomyelinase. Implications for Alzheimer's disease

J Biol Chem. 2004 Dec 3;279(49):51451-9. doi: 10.1074/jbc.M404635200. Epub 2004 Sep 27.

Abstract

Alzheimer's disease is a major illness of dementia characterized by the presence of amyloid plaques, neurofibrillary tangles, and extensive neuronal apoptosis. However, the mechanism behind neuronal apoptosis in the Alzheimer's-diseased brain is poorly understood. This study underlines the importance of neutral sphingomyelinase in fibrillar Abeta peptide-induced apoptosis and cell death in human primary neurons. Abeta1-42 peptides induced the activation of sphingomyelinases and the production of ceramide in neurons. Interestingly, neutral (N-SMase), but not acidic (A-SMase), sphingomyelinase was involved in Abeta1-42-mediated neuronal apoptosis and cell death. Abeta1-42-induced production of ceramide was redox-sensitive, as reactive oxygen species were involved in the activation of N-SMase but not A-SMase. Abeta1-42 peptides induced the NADPH oxidase-mediated production of superoxide radicals in neurons that was involved in the activation of N-SMase, but not A-SMase, via hydrogen peroxide. Consistently, superoxide radicals generated by hypoxanthine and xanthine oxidase also induced the activation of N-SMase, but not A-SMase, through a catalase-sensitive pathway. Furthermore, antisense knockdown of p22phox, a subunit of NADPH oxidase, inhibited Abeta1-42-induced neuronal apoptosis and cell death. These studies suggest that fibrillar Abeta1-42 peptides induce neuronal apoptosis through the NADPH oxidase-superoxide-hydrogen peroxide-NS-Mase-ceramide pathway.

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Alzheimer Disease / metabolism*
  • Amyloid beta-Peptides / chemistry
  • Amyloid beta-Peptides / physiology*
  • Apoptosis
  • Cell Survival
  • Cells, Cultured
  • Ceramides / chemistry
  • Ceramides / metabolism
  • DNA / chemistry
  • Diacylglycerol Kinase / metabolism
  • Enzyme Activation
  • Humans
  • Hydrogen Peroxide / chemistry
  • Hydrogen Peroxide / pharmacology
  • Hypoxanthine / chemistry
  • In Situ Nick-End Labeling
  • Lipids / chemistry
  • Membrane Transport Proteins / metabolism
  • NADPH Dehydrogenase / metabolism
  • NADPH Oxidases / metabolism*
  • Neurons / metabolism*
  • Oligonucleotides, Antisense / chemistry
  • Oxidation-Reduction
  • Oxygen / metabolism
  • Peptide Fragments / chemistry
  • Peptide Fragments / physiology*
  • Peptides / chemistry*
  • Phosphoproteins / metabolism
  • Reactive Oxygen Species
  • Sphingomyelin Phosphodiesterase / metabolism*
  • Superoxides / chemistry
  • Time Factors
  • Xanthine Oxidase / chemistry

Substances

  • Amyloid beta-Peptides
  • Ceramides
  • Lipids
  • Membrane Transport Proteins
  • Oligonucleotides, Antisense
  • Peptide Fragments
  • Peptides
  • Phosphoproteins
  • Reactive Oxygen Species
  • amyloid beta-protein (1-42)
  • Superoxides
  • Hypoxanthine
  • DNA
  • Hydrogen Peroxide
  • Xanthine Oxidase
  • NADPH Oxidases
  • CYBA protein, human
  • NADPH Dehydrogenase
  • Diacylglycerol Kinase
  • Sphingomyelin Phosphodiesterase
  • Oxygen