Vav1 and vav3 have critical but redundant roles in mediating platelet activation by collagen

J Biol Chem. 2004 Dec 24;279(52):53955-62. doi: 10.1074/jbc.M410355200. Epub 2004 Sep 27.

Abstract

Vav family proteins are guanine nucleotide exchange factors for the Rho/Rac family of small GTP-binding proteins. In addition, they have domains that mediate protein-protein interactions, including one Src homology 2 (SH2) and two Src homology 3 (SH3) domains. Vav1, Vav2, and Vav3 play a crucial role in the regulation of phospholipase C gamma (PLC gamma) isoforms by immuno-tyrosine-based activation motif (ITAM)-coupled receptors, including the T- and B-cell antigen receptors. We have reported in platelets, however, that Vav1 and Vav2 are not required for activation of PLC gamma 2 in response to stimulation of the ITAM-coupled collagen receptor glycoprotein VI (GPVI). Here we report that Vav3 is tyrosinephosphorylated upon activation of GPVI but that Vav3-deficient platelets also exhibit a normal response upon activation of the ITAM receptor. In sharp contrast, platelets deficient in both Vav1 and Vav3 show a marked inhibition of aggregation and spreading upon activation of GPVI, which is associated with a reduction in tyrosine phosphorylation of PLC gamma 2. The phenotype of Vav1/2/3 triple-deficient platelets is similar to that of Vav1/3 double-deficient cells. These results demonstrate that Vav3 and Vav1 play crucial but redundant roles in the activation of PLC gamma 2 by GPVI. This is the first time that absolute redundancy between two protein isoforms has been observed with respect to the regulation of PLC gamma 2 in platelets.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Agammaglobulinaemia Tyrosine Kinase
  • Animals
  • Blood Platelets / chemistry
  • Blood Platelets / physiology
  • CD36 Antigens / chemistry
  • CD36 Antigens / physiology
  • Cell Cycle Proteins
  • Collagen / pharmacology*
  • Enzyme Activation / physiology
  • Enzyme Precursors / metabolism
  • Guanine Nucleotide Exchange Factors
  • Humans
  • Intracellular Signaling Peptides and Proteins
  • Mice
  • Mice, Knockout
  • Oncogene Proteins / deficiency
  • Oncogene Proteins / genetics
  • Oncogene Proteins / physiology
  • Phospholipase C gamma
  • Phosphorylation
  • Phosphotyrosine / metabolism
  • Platelet Activation / drug effects*
  • Platelet Activation / physiology
  • Protein-Tyrosine Kinases / metabolism
  • Proto-Oncogene Proteins
  • Proto-Oncogene Proteins c-vav
  • Receptors, Collagen / chemistry
  • Receptors, Collagen / physiology
  • Syk Kinase
  • Type C Phospholipases / metabolism
  • src-Family Kinases / metabolism

Substances

  • CD36 Antigens
  • Cell Cycle Proteins
  • Enzyme Precursors
  • Guanine Nucleotide Exchange Factors
  • Intracellular Signaling Peptides and Proteins
  • Oncogene Proteins
  • Proto-Oncogene Proteins
  • Proto-Oncogene Proteins c-vav
  • Receptors, Collagen
  • VAV1 protein, human
  • VAV3 protein, human
  • Vav1 protein, mouse
  • Vav2 protein, mouse
  • Vav3 protein, mouse
  • Phosphotyrosine
  • Collagen
  • Protein-Tyrosine Kinases
  • Agammaglobulinaemia Tyrosine Kinase
  • SYK protein, human
  • Syk Kinase
  • Syk protein, mouse
  • src-Family Kinases
  • Type C Phospholipases
  • Phospholipase C gamma