How to evaluate phenotype-genotype relationship in rare coagulation haemorrhagic disorders: examples from FVII deficiency

Haemophilia. 2004 Oct:10 Suppl 4:177-9. doi: 10.1111/j.1365-2516.2004.00989.x.

Abstract

The study of the molecular pathogenesis of several single-gene disorders, such as coagulation-factor deficiencies, has revealed the variability of phenotypic expression, even of the same mutations in single genes. These studies underline the complexity of research dealing with the definition of the molecular bases of disorders. Sequence variations provide only the starting point to define pathological genotype-phenotype relationships.

Publication types

  • Review

MeSH terms

  • Blood Coagulation Disorders / complications
  • Blood Coagulation Disorders / congenital
  • Blood Coagulation Disorders / genetics*
  • Blood Coagulation Factors / genetics
  • Factor VII Deficiency / complications
  • Factor VII Deficiency / genetics*
  • Genotype
  • Hemorrhage / etiology
  • Hemorrhage / genetics*
  • Humans
  • Mutation
  • Phenotype
  • Polymorphism, Genetic

Substances

  • Blood Coagulation Factors