T-cell receptor variable region gene expression in cutaneous T-cell lymphomas

J Cutan Pathol. 1992 Feb;19(1):21-6. doi: 10.1111/j.1600-0560.1992.tb01554.x.

Abstract

The cutaneous T-cell lymphomas (CTCL) are a group of diseases characterized by malignant proliferations of CD4 positive T-cells having monoclonally rearranged T-cell receptor (TCR) genes. A recent study using monoclonal antibodies to two TCR beta-chain variable (V) region gene products showed preferential expression of the V beta 8 gene product in these tumors. The finding of predominant usage of a single V beta gene would imply that selection by antigen is important in the etiology of these tumors. We have studied eight cases of cutaneous T-cell lymphoma and one cell line derived from a patient with mycosis fungoides/Sezary syndrome, using an extended panel of antibodies to V region gene products. Contrary to the previous report, in our study expression of the V beta 8 gene product by tumor cells was not observed in any of the cases of CTCL or in the tumor cell line studied; preferential use of any of the variable region genes recognized by the antibodies in the panel was not observed.

MeSH terms

  • Adult
  • Aged
  • Aged, 80 and over
  • Antibodies, Monoclonal
  • Base Sequence
  • Female
  • Gene Expression Regulation, Neoplastic / physiology*
  • Gene Rearrangement, T-Lymphocyte / genetics
  • Humans
  • Lymphoma, T-Cell, Cutaneous / genetics*
  • Lymphoma, T-Cell, Cutaneous / physiopathology
  • Lymphoma, T-Cell, Cutaneous / ultrastructure
  • Male
  • Middle Aged
  • Molecular Sequence Data
  • Receptors, Antigen, T-Cell / genetics*
  • Sezary Syndrome / genetics
  • Sezary Syndrome / physiopathology
  • Skin Neoplasms / genetics*
  • Skin Neoplasms / physiopathology
  • Skin Neoplasms / ultrastructure

Substances

  • Antibodies, Monoclonal
  • Receptors, Antigen, T-Cell