Objective: To describe a unique case of descending salpingitis and functioning endometrium in a noncavitated mullerian remnant in a patient with Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome.
Design: Case report.
Setting: Second Department of Obstetrics and Gynecology, University of Athens, Aretaieion Hospital, Athens, Greece.
Patient(s): A 25-year-old patient with MRKH syndrome who presented with lower abdominal pain.
Intervention(s): Clinical examination, transabdominal ultrasonography, laparoscopy, laparotomy.
Main outcome measure(s): Clinical symptoms of salpingitis and hematometra; laparoscopic and laboratory confirmation.
Result(s): Laparoscopy revealed an infection of the right salpinx, and surgical excision by laparotomy revealed a noncanalized mullerian remnant with functioning endometrium.
Conclusion(s): Salpingitis can present in patients with MRKH syndrome. Probable presence of functioning endometrium must be taken under consideration.