Hemoglobin C modulates the surface topography of Plasmodium falciparum-infected erythrocytes

J Struct Biol. 2005 May;150(2):163-9. doi: 10.1016/j.jsb.2005.02.008.

Abstract

There is a well-established clinical association between hemoglobin genotype and innate protection against Plasmodium falciparum malaria. In contrast to normal hemoglobin A, mutant hemoglobin C is associated with substantial reductions in the risk of severe malaria in both heterozygous AC and homozygous CC individuals. Irrespective of hemoglobin genotype, parasites may induce knob-like projections on the erythrocyte surface. The knobs play a major role in the pathogenesis of severe malaria by serving as points of adherence for P. falciparum-infected erythrocytes to microvascular endothelia. To evaluate the influence of hemoglobin genotype on knob formation, we used a combination of atomic force and light microscopy for concomitant topographic and wide-field fluorescence imaging. Parasitized AA, AC, and CC erythrocytes showed a population of knobs with a mean width of approximately 70 nm. Parasitized AC and CC erythrocytes showed a second population of large knobs with a mean width of approximately 120 nm. Furthermore, spatial knob distribution analyses demonstrated that knobs on AC and CC erythrocytes were more aggregated than on AA erythrocytes. These data support a model in which large knobs and their aggregates are promoted by hemoglobin C, reducing the adherence of parasitized erythrocytes in the microvasculature and ameliorating the severity of a malaria infection.

MeSH terms

  • Animals
  • Cell Adhesion
  • Cell Shape
  • Endothelium, Vascular
  • Erythrocytes / parasitology*
  • Erythrocytes / pathology
  • Genotype
  • Hemoglobin C / genetics
  • Hemoglobin C / physiology*
  • Humans
  • Malaria, Falciparum / blood
  • Malaria, Falciparum / etiology
  • Microcirculation
  • Microscopy, Atomic Force
  • Plasmodium falciparum / pathogenicity*
  • Surface Properties

Substances

  • Hemoglobin C