"Man-in-the-barrel" syndrome as delayed manifestation of extrapontine and central pontine myelinolysis: beneficial effect of intravenous immunoglobulin

J Neurol Sci. 2005 Oct 15;237(1-2):103-6. doi: 10.1016/j.jns.2005.05.012.

Abstract

"Man-in-the-barrel" syndrome has been rarely described following osmotic myelinolysis. We report a case of a 45-year-old woman admitted with septicemia and severe hyponatremia. She presented with a "man-in-the-barrel" syndrome which developed more than 10 days after rapid correction of the hyponatremia. There was radiological evidence of central pontine and extrapontine myelinolysis. Three days after completing a course of intravenous immunoglobulin therapy (0.4 g/kg body weight/day for 5 days) there was considerable improvement (Expanded Disability Status Scale score improved 30%). This case, reported for its peculiar mode of development, unusual presentation and challenging therapeutic response to intravenous immunoglobulin, highlights the enigmatic and unpredictable aspects of osmotic myelinolysis.

Publication types

  • Case Reports

MeSH terms

  • Arm
  • Brain / pathology
  • Female
  • Humans
  • Hyponatremia / blood
  • Immunization, Passive*
  • Immunoglobulins, Intravenous / therapeutic use*
  • Magnetic Resonance Imaging
  • Middle Aged
  • Myelinolysis, Central Pontine / complications*
  • Myelinolysis, Central Pontine / pathology
  • Myelinolysis, Central Pontine / therapy*
  • Paralysis / etiology*
  • Paralysis / pathology
  • Paralysis / therapy*
  • Sepsis / complications
  • Sodium / blood
  • Water-Electrolyte Balance / physiology

Substances

  • Immunoglobulins, Intravenous
  • Sodium