State of the Art and Future Needs in Cytogenetic/Molecular Genetics/Arrays in childhood lymphoma: summary report of workshop at the First International Symposium on childhood and adolescent non-Hodgkin lymphoma, April 9, 2003, New York City, NY

Pediatr Blood Cancer. 2005 Oct 15;45(5):616-22. doi: 10.1002/pbc.20552.

Abstract

Background: A significant number of studies describe the cytogenetics and molecular genetics of adult non-Hodgkin lymphoma (NHL); however, similar knowledge is lacking regarding pediatric NHL.

Methods: A workshop to discuss the "State of the Art and Future Needs in Cytogenetic/Molecular Genetics/Arrays" in pediatric NHL was held in conjunction with the First International Symposium on Childhood and Adolescent Non-Hodgkin Lymphoma on April 9, 2003 in New York City.

Results: Cytogenetic characteristics of pediatric NHL include 14q11.2 rearrangements in T-cell lymphoblastic leukemia/lymphomas (LBL), ALK rearrangements in anaplastic large cell lymphomas (ALCL), and CMYC translocations in both Burkitt and Burkitt-like lymphomas (BL/BLL). Pediatric diffuse large B-cell lymphoma (DLBCL) is cytogenetically different from DLBCL in adults, suggesting a different disease in children. Microarray studies demonstrate three types of T-cell leukemia, the leukemic counterpart of LBL, that block T-cell differentiation at different stages of T-cell development, corresponding to LYL, TAL1, and HOX-expressing leukemias. ALCL cell lines have a unique expression profile compared to normal T-cells. Germinal centers of BL have CMYC expression signatures, indicating that CMYC expression is ectopic and does not reflect the physiology of the normal cell counterpart.

Conclusions: Additional cytogenetic, molecular and microarray investigations of NHL in children are vital to better understand these diseases, their etiology, and differences from adult NHL. A greater understanding of pediatric NHL will lead to disease-specific and patient-individualized therapies of these diseases.

Publication types

  • Congress
  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Adolescent
  • Basic Helix-Loop-Helix Transcription Factors
  • Burkitt Lymphoma / genetics
  • Child
  • Cytogenetic Analysis
  • DNA-Binding Proteins / genetics
  • Gene Rearrangement
  • Homeodomain Proteins / genetics
  • Humans
  • Intracellular Signaling Peptides and Proteins
  • Lymphoma, B-Cell / genetics
  • Lymphoma, Large B-Cell, Diffuse / genetics
  • Lymphoma, Non-Hodgkin / genetics*
  • Microarray Analysis
  • Molecular Biology
  • Neoplasm Proteins / genetics
  • Oncogene Proteins / genetics
  • Oncogene Proteins, Fusion / genetics

Substances

  • Basic Helix-Loop-Helix Transcription Factors
  • DNA-Binding Proteins
  • Homeodomain Proteins
  • Intracellular Signaling Peptides and Proteins
  • LYL1 protein, human
  • Neoplasm Proteins
  • Oncogene Proteins
  • Oncogene Proteins, Fusion
  • STIL protein, human
  • TLX3 protein, human