Palmoplantar keratoderma with sclerodactyly (Huriez syndrome)

A Patrizi; V Di Lernia; P Patrone

doi:10.1016/0190-9622(92)70121-u

Palmoplantar keratoderma with sclerodactyly (Huriez syndrome)

J Am Acad Dermatol. 1992 May;26(5 Pt 2):855-7. doi: 10.1016/0190-9622(92)70121-u.

Authors

A Patrizi¹, V Di Lernia, P Patrone

Affiliation

¹ Department of Dermatology, University of Bologna, Italy.

PMID: 1613149
DOI: 10.1016/0190-9622(92)70121-u

Abstract

A syndrome characterized by palmoplantar keratoderma, sclerodactyly, and skin cancer was first described in two families by Huriez et al. The pattern of inheritance was compatible with that of an autosomal dominant disorder. We report a patient with this condition and review the literature.

Publication types

Case Reports
Review

MeSH terms

Fingers*
Humans
Keratoderma, Palmoplantar, Diffuse / complications
Keratoderma, Palmoplantar, Diffuse / diagnosis*
Male
Middle Aged
Nails, Malformed*
Scleroderma, Localized / complications
Scleroderma, Localized / diagnosis*
Syndrome