Myhre syndrome in a female with previously undescribed symptoms: further delineation of the phenotype

Am J Med Genet A. 2005 Dec 1;139A(2):127-30. doi: 10.1002/ajmg.a.30988.

Abstract

Myhre syndrome is a rare connective tissue disease characterized by nonprogressive stiffness of the large joints, short stature with a peculiar build, and a distinctive facial phenotype. Developmental delay is common. Three female patients have so far been described. Here, we report on a 16-year-old female with Myhre syndrome. She has vertebral defects, hypertrophic scar formation, and a stiff skin in addition to the features that have previously been reported in association with Myhre syndrome.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Abdomen / diagnostic imaging
  • Bone and Bones / diagnostic imaging
  • Connective Tissue Diseases / genetics
  • Connective Tissue Diseases / pathology*
  • Connective Tissue Diseases / physiopathology
  • Echocardiography
  • Female
  • Humans
  • Karyotyping
  • Phenotype
  • Radiography
  • Syndrome