A MAPK/HNRPK pathway controls BCR/ABL oncogenic potential by regulating MYC mRNA translation

Blood. 2006 Mar 15;107(6):2507-16. doi: 10.1182/blood-2005-09-3732. Epub 2005 Nov 17.

Abstract

Altered mRNA translation is one of the effects exerted by the BCR/ABL oncoprotein in the blast crisis phase of chronic myelogenous leukemia (CML). Here, we report that in BCR/ABL+ cell lines and in patient-derived CML blast crisis mononuclear and CD34+ cells, p210(BCR/ABL) increases expression and activity of the transcriptional-inducer and translational-regulator heterogeneous nuclear ribonucleoprotein K (hnRNP K or HNRPK) in a dose- and kinase-dependent manner through the activation of the MAPK(ERK1/2) pathway. Furthermore, HNRPK down-regulation and interference with HNRPK translation-but not transcription-regulatory activity impairs cytokine-independent proliferation, clonogenic potential, and in vivo leukemogenic activity of BCR/ABL-expressing myeloid 32Dcl3 and/or primary CD34+ CML-BC patient cells. Mechanistically, we demonstrate that decreased internal ribosome entry site (IRES)-dependent Myc mRNA translation accounts for the phenotypic changes induced by inhibition of the BCR/ABL-ERK-dependent HNRPK translation-regulatory function. Accordingly, MYC protein but not mRNA levels are increased in the CD34+ fraction of patients with CML in accelerated and blastic phase but not in chronic phase CML patients and in the CD34+ fraction of marrow cells from healthy donors. Thus, BCR/ABL-dependent enhancement of HNRPK translation-regulation is important for BCR/ABL leukemogenesis and, perhaps, it might contribute to blast crisis transformation.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, Non-P.H.S.

MeSH terms

  • Antigens, CD34
  • Blast Crisis / etiology
  • Cell Line, Tumor
  • Fusion Proteins, bcr-abl / physiology*
  • Heterogeneous-Nuclear Ribonucleoprotein K
  • Humans
  • Leukemia, Myelogenous, Chronic, BCR-ABL Positive / etiology*
  • Mitogen-Activated Protein Kinases / metabolism*
  • Protein Biosynthesis*
  • Proto-Oncogene Proteins c-myc / genetics*
  • RNA, Messenger / genetics
  • Ribonucleoproteins / metabolism*
  • Tumor Cells, Cultured

Substances

  • Antigens, CD34
  • Heterogeneous-Nuclear Ribonucleoprotein K
  • MYC protein, human
  • Proto-Oncogene Proteins c-myc
  • RNA, Messenger
  • Ribonucleoproteins
  • HNRNPK protein, human
  • Fusion Proteins, bcr-abl
  • Mitogen-Activated Protein Kinases