Hepatitis C virus protease NS3/4A cleaves mitochondrial antiviral signaling protein off the mitochondria to evade innate immunity

Proc Natl Acad Sci U S A. 2005 Dec 6;102(49):17717-22. doi: 10.1073/pnas.0508531102. Epub 2005 Nov 21.

Abstract

Hepatitis C virus (HCV) is a global epidemic manifested mainly by chronic infection. One strategy that HCV employs to establish chronic infection is to use the viral Ser protease NS3/4A to cleave some unknown cellular targets involved in innate immunity. Here we show that the target of NS3/4A is the mitochondrial antiviral signaling protein, MAVS, that activates NF-kappaB and IFN regulatory factor 3 to induce type-I interferons. NS3/4A cleaves MAVS at Cys-508, resulting in the dislocation of the N-terminal fragment of MAVS from the mitochondria. Remarkably, a point mutation of MAVS at Cys-508 renders MAVS resistant to cleavage by NS3/4A, thus maintaining the ability of MAVS to induce interferons in HCV replicon cells. NS3/4A binds to and colocalizes with MAVS in the mitochondrial membrane, and it can cleave MAVS directly in vitro. These results provide an example of host-pathogen interaction in which the virus evades innate immunity by dislodging a pivotal antiviral protein from the mitochondria and suggest that blocking the cleavage of MAVS by NS3/4A may be applied to the prevention and treatment of HCV.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Sequence
  • Carrier Proteins / chemistry
  • Carrier Proteins / metabolism*
  • Cell Line
  • Cysteine / genetics
  • Cysteine / metabolism
  • Hepacivirus / enzymology*
  • Hepacivirus / immunology*
  • Hepacivirus / physiology
  • Humans
  • Immunity, Innate / drug effects
  • Immunity, Innate / immunology*
  • Interferon-beta / pharmacology
  • Intracellular Signaling Peptides and Proteins
  • Mitochondria / drug effects
  • Mitochondria / metabolism*
  • Mitochondrial Proteins / metabolism*
  • Molecular Sequence Data
  • Protein Binding
  • Sequence Alignment
  • Signal Transduction / drug effects
  • Viral Nonstructural Proteins / chemistry
  • Viral Nonstructural Proteins / metabolism*
  • Viral Proteins / chemistry
  • Viral Proteins / metabolism*
  • Virus Replication

Substances

  • Carrier Proteins
  • Intracellular Signaling Peptides and Proteins
  • Mitochondrial Proteins
  • NS3 protein, hepatitis C virus
  • NS4A cofactor peptide, Hepatitis C virus
  • Viral Nonstructural Proteins
  • Viral Proteins
  • Interferon-beta
  • Cysteine