This is a report of an extremely rare case of cavernous hemangioma over the anterior fontanelle in a 5-year-old boy. Cavernous hemangioma is most common in or beneath the skin of the face, neck, and extremities and sometimes occurs in the scalp. Although cavernous hemangioma is often quoted in the literature as a differential diagnosis of a mass located at the anterior fontanelle, we could not find an illustrative case in published articles. We discuss the characteristics and differential diagnosis of cavernous hemangioma over the anterior fontanelle.