Association of the PTPN22*R620W polymorphism with autoimmune myasthenia gravis

Ann Neurol. 2006 Feb;59(2):404-7. doi: 10.1002/ana.20751.

Abstract

Objective: Our objective was to investigate a role of the intracellular tyrosine phosphatase PTPN22*R620W variant in autoimmune myasthenia gravis (MG), considering disease heterogeneity.

Methods: We used a case-control design, comparing 470 patients and 296 controls, all French whites. Patients were categorized depending on the presence of a thymoma and serum anti-titin antibodies.

Results: The 620W risk allele was increased in 293 nonthymoma patients without anti-titin antibodies (odds ratio, 1.97; 95% confidence interval, 1.32-2.97, p = 0.00059) but not in nonthymoma patients with anti-titin antibodies or in thymoma patients.

Interpretation: Our genetic findings strengthen the concept that these groups of patients correspond to etiologically distinct disease entities.

Publication types

  • Comparative Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Aged
  • Alleles
  • Arginine / genetics*
  • Confidence Intervals
  • Connectin
  • DNA Mutational Analysis / methods
  • Female
  • Gene Frequency
  • Genetic Predisposition to Disease*
  • Humans
  • Male
  • Middle Aged
  • Muscle Proteins / metabolism
  • Myasthenia Gravis / classification
  • Myasthenia Gravis / genetics*
  • Odds Ratio
  • Polymorphism, Genetic*
  • Protein Kinases / metabolism
  • Protein Tyrosine Phosphatase, Non-Receptor Type 22
  • Protein Tyrosine Phosphatases / genetics*
  • Tryptophan / genetics*

Substances

  • Connectin
  • Muscle Proteins
  • TTN protein, human
  • Tryptophan
  • Arginine
  • Protein Kinases
  • PTPN22 protein, human
  • Protein Tyrosine Phosphatase, Non-Receptor Type 22
  • Protein Tyrosine Phosphatases