Truncated PrP(c) in mammalian brain: interspecies variation and location in membrane rafts

Biol Chem. 2006 Mar;387(3):297-300. doi: 10.1515/BC.2006.039.

Abstract

A key molecular event in prion diseases is the conversion of cellular prion protein (PrP(c)) into an abnormal misfolded conformer (PrP(sc)). The PrP(c) N-terminal domain plays a central role in PrP(c) functions and in prion propagation. Because mammalian PrP(c) is found as a full-length and N-terminally truncated form, we examined the presence and amount of PrP(c) C-terminal fragment in the brain of different species. We found important variations between primates and rodents. In addition, our data show that the PrP(c) fragment is present in detergent-resistant raft domains, a membrane domain of critical importance for PrP(c) functions and its conversion into PrP(sc).

MeSH terms

  • Animals
  • Brain / metabolism*
  • Cell Membrane / metabolism*
  • Cricetinae
  • Detergents / pharmacology
  • Electrophoresis, Polyacrylamide Gel
  • Membrane Microdomains / metabolism*
  • Papio
  • PrPC Proteins / chemistry
  • PrPC Proteins / genetics
  • PrPC Proteins / metabolism*
  • PrPSc Proteins / chemistry
  • PrPSc Proteins / genetics
  • PrPSc Proteins / metabolism*
  • Primates
  • Prion Diseases / etiology
  • Prion Diseases / metabolism*
  • Rodentia
  • Species Specificity

Substances

  • Detergents
  • PrPC Proteins
  • PrPSc Proteins