Ovarian adrenal rest tissue in congenital adrenal hyperplasia--a patient report

H L Claahsen-van der Grinten; C A Hulsbergen-van de Kaa; B J Otten

doi:10.1515/jpem.2006.19.2.177

Ovarian adrenal rest tissue in congenital adrenal hyperplasia--a patient report

J Pediatr Endocrinol Metab. 2006 Feb;19(2):177-82. doi: 10.1515/jpem.2006.19.2.177.

Authors

H L Claahsen-van der Grinten¹, C A Hulsbergen-van de Kaa, B J Otten

Affiliation

¹ Department of Metabolic and Endocrine Disease and Radboud University, Nijmegen Medical Center, The Netherlands. [email protected]

PMID: 16562593
DOI: 10.1515/jpem.2006.19.2.177

Abstract

We report a young girl who died in an Addisonian crisis due to previously undiagnosed congenital adrenal hyperplasia (CAH), in whom ovarian adrenal rest tissue was detected at postmortem histopathological examination. This is a very rare complication in female patients with CAH with only two previously reported cases.

Publication types

Case Reports

MeSH terms

Addison Disease / complications*
Addison Disease / pathology
Adrenal Hyperplasia, Congenital / complications*
Adrenal Hyperplasia, Congenital / pathology
Adrenal Rest Tumor / complications*
Adrenal Rest Tumor / pathology
Fatal Outcome
Female
Humans
Infant
Ovarian Neoplasms / complications*
Ovarian Neoplasms / pathology