Transcriptional repressor Blimp-1 is essential for T cell homeostasis and self-tolerance

Nat Immunol. 2006 May;7(5):466-74. doi: 10.1038/ni1321. Epub 2006 Mar 26.

Abstract

T cell homeostasis is crucial for a functional immune system, as the accumulation of T cells resulting from lack of regulatory T cells or an inability to shut down immune responses can lead to inflammation and autoimmune pathology. Here we show that Blimp-1, a transcriptional repressor that is a 'master regulator' of terminal B cell differentiation, was expressed in a subset of antigen-experienced CD4(+) and CD8(+) T cells. Mice reconstituted with fetal liver stem cells expressing a mutant Blimp-1 lacking the DNA-binding domain developed a lethal multiorgan inflammatory disease caused by an accumulation of effector and memory T cells. These data identify Blimp-1 as an essential regulator of T cell homeostasis and suggest that Blimp-1 regulates both B cell and T cell differentiation.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Apoptosis
  • B-Lymphocytes / immunology*
  • Cell Differentiation
  • Down-Regulation / immunology*
  • Homeostasis / immunology*
  • Immunologic Memory / drug effects
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • Mice, Transgenic
  • Positive Regulatory Domain I-Binding Factor 1
  • Repressor Proteins / genetics
  • Repressor Proteins / metabolism*
  • Repressor Proteins / pharmacology
  • Self Tolerance / immunology*
  • T-Lymphocytes / cytology
  • T-Lymphocytes / immunology*
  • Transcription Factors / genetics
  • Transcription Factors / metabolism*
  • Transcription Factors / pharmacology

Substances

  • Prdm1 protein, mouse
  • Repressor Proteins
  • Transcription Factors
  • Positive Regulatory Domain I-Binding Factor 1