Precursor B lymphoblastic leukemia 32 months after local therapy for a primary extramedullary myeloid cell tumor

Pediatr Blood Cancer. 2007 Dec;49(7):1039-46. doi: 10.1002/pbc.20789.

Abstract

A primary extramedullary myeloid cell tumor (pEMT) of an inguinal lymph node was completely excised without subsequent anti-tumor therapy in a 6-year-old child. Clinical observation and monitoring of blood and bone marrow (BM) did not reveal any pathologic results before 32 months, when a precursor B lymphoblastic leukemia was diagnosed. Identical T-cell receptor gamma rearrangement in nodal pEMT and in precursor B lymphoblastic leukemia in BM indicates a clonal relationship of these two tumors.

Publication types

  • Case Reports

MeSH terms

  • Acute Disease
  • Antigens, Neoplasm / biosynthesis
  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use
  • Biomarkers, Tumor / biosynthesis
  • Bone Marrow / pathology
  • Child
  • Cytogenetic Analysis
  • Female
  • Flow Cytometry
  • Follow-Up Studies
  • Humans
  • Immunophenotyping
  • Neoplasms, Second Primary / diagnosis
  • Neoplasms, Second Primary / immunology
  • Neoplasms, Second Primary / therapy*
  • Polymerase Chain Reaction / methods
  • Precursor B-Cell Lymphoblastic Leukemia-Lymphoma / diagnosis*
  • Precursor B-Cell Lymphoblastic Leukemia-Lymphoma / genetics
  • Precursor B-Cell Lymphoblastic Leukemia-Lymphoma / immunology
  • Receptors, Antigen, T-Cell, gamma-delta / biosynthesis
  • Receptors, Antigen, T-Cell, gamma-delta / genetics
  • Remission Induction
  • Sarcoma, Myeloid / diagnosis
  • Sarcoma, Myeloid / immunology
  • Sarcoma, Myeloid / therapy*
  • Time Factors
  • Treatment Outcome

Substances

  • Antigens, Neoplasm
  • Biomarkers, Tumor
  • Receptors, Antigen, T-Cell, gamma-delta