Prenatal diagnosis of de novo deletions of 8p23.1 or 15q26.1 in two fetuses with diaphragmatic hernia and congenital heart defects

Prenat Diagn. 2006 Jun;26(6):577-80. doi: 10.1002/pd.1468.

Abstract

Objective: To show the importance of using high-resolution chromosome analysis and FISH-technique for finding subtle chromosomal lesions in prenatal diagnosis specially when there are abnormal ultrasound findings.

Methods: Ecographic examination of the fetus. GTG banded chromosome and FISH analysis using subtelomeric probes on amniocytes.

Results: We report two prenatal cases with congenital diaphragmatic hernia (CDH) and congenital heart defects (CHDs) with different deletions confirmed by FISH: del(8)(p23.1p23.1) and del(15)(q26.1).

Conclusion: These cases support the evidence that the regions 15q26.1 and 8p23.1 may play an important role in the development of the diaphragm. A deletion 8p23.1 or 15q26.1 should be considered whenever a CDH and/or a cardiac abnormality are detected on ultrasound.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple
  • Adult
  • Chromosome Banding
  • Chromosome Deletion*
  • Chromosomes, Human, Pair 15*
  • Chromosomes, Human, Pair 8*
  • Female
  • Fetal Diseases / diagnosis
  • Fetal Diseases / genetics
  • Heart Defects, Congenital / complications
  • Heart Defects, Congenital / diagnosis*
  • Heart Defects, Congenital / embryology
  • Heart Defects, Congenital / genetics
  • Hernia, Diaphragmatic / complications
  • Hernia, Diaphragmatic / diagnosis*
  • Hernia, Diaphragmatic / embryology
  • Hernia, Diaphragmatic / genetics
  • Humans
  • In Situ Hybridization, Fluorescence
  • Pregnancy
  • Prenatal Diagnosis* / methods