ASPP2 is a haploinsufficient tumor suppressor that cooperates with p53 to suppress tumor growth

Genes Dev. 2006 May 15;20(10):1262-7. doi: 10.1101/gad.374006.

Abstract

ASPP2 stimulates the apoptotic function of the p53 family in vivo. We show here that ASPP2-/- pups died before weaning. This postnatal lethality was significantly enhanced in p53+/- background and both deletions are synthetic lethal. ASPP2+/- mice developed spontaneous tumors. The tumor onset was accelerated by gamma-irradiation or in p53+/- background. Tumors derived from ASPP2+/- mice retained wild-type ASPP2 allele even though some of them lost p53. These provide the first genetic evidence that ASPP2 is a haploinsufficient tumor suppressor that shares overlapping function(s) with p53 in mouse development and tumor suppression.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Alleles
  • Animals
  • Genes, Lethal
  • Genes, Tumor Suppressor*
  • Haploidy
  • Heterozygote
  • Lymphoma / genetics*
  • Mice
  • Mice, Mutant Strains
  • Mutation
  • Tumor Suppressor Protein p53 / genetics*
  • Tumor Suppressor Proteins / genetics*

Substances

  • Trp53bp2 protein, mouse
  • Tumor Suppressor Protein p53
  • Tumor Suppressor Proteins