Diagnostic evaluation of clinically normal subjects with chronic hyperCKemia

Neurology. 2006 May 23;66(10):1585-7. doi: 10.1212/01.wnl.0000216144.69630.6e.

Abstract

The authors analyzed muscle biopsy specimens of 104 patients with creatine kinase activity greater than 500 UI/L (normal 10 to 170 UI/L) without signs of muscle weakness. They achieved a definite or probable diagnosis in 55% of cases. The most frequently identified diseases were glycogen storage diseases, muscular dystrophies, and inflammatory myopathies. The probability of making a diagnosis was higher in children and when creatine kinase level was greater than 2,000 UI/L.

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Biomarkers
  • Biopsy
  • Child
  • Child, Preschool
  • Cohort Studies
  • Creatine Kinase, MM Form / blood*
  • Dystrophin / deficiency
  • Fatigue / blood
  • Fatigue / etiology
  • Female
  • Glycogen Storage Disease Type II / blood
  • Glycogen Storage Disease Type II / diagnosis
  • Glycogen Storage Disease Type V / blood
  • Glycogen Storage Disease Type V / diagnosis
  • Humans
  • Male
  • Middle Aged
  • Muscle Cramp / blood
  • Muscle Cramp / etiology
  • Muscle, Skeletal / enzymology
  • Muscle, Skeletal / pathology
  • Neuromuscular Diseases / blood*
  • Neuromuscular Diseases / diagnosis
  • Retrospective Studies

Substances

  • Biomarkers
  • Dystrophin
  • Creatine Kinase, MM Form