Array CGH profiling of favourable histology Wilms tumours reveals novel gains and losses associated with relapse

J Pathol. 2006 Sep;210(1):49-58. doi: 10.1002/path.2021.

Abstract

Despite the excellent survival of Wilms tumour patients treated with multimodality therapy, approximately 15% will suffer from tumour relapse, where response rates are markedly reduced. We have carried out microarray-based comparative genomic hybridisation on a series of 76 Wilms tumour samples, enriched for cases which recurred, to identify changes in DNA copy number associated with clinical outcome. Using 1Mb-spaced genome-wide BAC arrays, the most significantly different genomic changes between favourable histology tumours that did (n = 37), and did not (n = 39), subsequently relapse were gains on 1q, and novel deletions at 12q24 and 18q21. Further relapse-associated loci included losses at 1q32.1, 2q36.3-2q37.1, and gain at 13q31. 1q gains correlated strongly with loss of 1p and/or 16q. In 3 of 11 cases with concurrent 1p(-)/1q(+), a breakpoint was identified at 1p13. Multiple low-level sub-megabase gains along the length of 1q were identified using chromosome 1 tiling-path arrays. One such recurrent region at 1q22-q23.1 included candidate genes RAB25, NES, CRABP2, HDGF and NTRK1, which were screened for mRNA expression using quantitative RT-PCR. These data provide a high-resolution catalogue of genomic copy number changes in relapsing favourable histology Wilms tumours.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Chromosome Aberrations
  • Chromosome Deletion
  • Chromosomes, Human, Pair 1 / genetics
  • Chromosomes, Human, Pair 16 / genetics
  • Chromosomes, Human, Pair 8 / genetics
  • DNA, Neoplasm / genetics
  • Genes, Wilms Tumor / physiology
  • Humans
  • Kidney Neoplasms / genetics*
  • Kidney Neoplasms / pathology
  • Neoplasm Recurrence, Local / genetics
  • Oligonucleotide Array Sequence Analysis / methods*
  • RNA, Messenger / analysis
  • RNA, Neoplasm / analysis
  • Treatment Outcome
  • Wilms Tumor / genetics*
  • Wilms Tumor / pathology

Substances

  • DNA, Neoplasm
  • RNA, Messenger
  • RNA, Neoplasm