4q35 deletion and 10p15 duplication associated with immunodeficiency

Am J Med Genet A. 2006 Oct 15;140(20):2231-5. doi: 10.1002/ajmg.a.31431.

Abstract

We report a familial cryptic reciprocal translocation between 4q35 and 10p15 leading to deletion of the terminal long arm of chromosome 4 and duplication of the terminal short arm of chromosome 10 in two family members who both have immunological disturbances and a similar facial appearance. The precise location and extent of the deletion and duplication was determined by fluorescence in situ hybridization (FISH). Furthermore, we investigated the deletion breakpoint of a previously reported patient with 4q34.3-qter deletion [Van Buggenhout et al. (2004); Am J Med Genet Part A 131A:186-189].

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple / genetics*
  • Abnormalities, Multiple / pathology
  • Adolescent
  • Adult
  • Chromosomes, Human, Pair 10 / genetics*
  • Chromosomes, Human, Pair 4 / genetics*
  • Female
  • Humans
  • Immunologic Deficiency Syndromes / genetics*
  • In Situ Hybridization, Fluorescence
  • Intellectual Disability / genetics*
  • Intellectual Disability / pathology
  • Pedigree
  • Phenotype*
  • Translocation, Genetic / genetics*