Abstract
The capacity of ganglioside-specific autoantibodies to recruit leukocyte effector functions was studied. Serum samples from 87 patients with Guillain-Barré (GBS) or Miller Fisher syndrome (MFS), containing GM1-, GQ1b-, or GD1b-specific IgG or IgA, were tested for leukocyte activating capacity. Ganglioside-specific IgG antibodies generally induced leukocyte activation, irrespective of specificity. The magnitude of leukocyte degranulation correlated with GM1- and GQ1b-specific IgG titers, but not with disease severity. Finally, GM1-specific IgA activated leukocytes through the IgA receptor, FcalphaRI (CD89). Therefore, both ganglioside-specific IgG and IgA can recruit leukocyte effector functions, which may be relevant in the pathogenesis of GBS and MFS.
Publication types
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Research Support, Non-U.S. Gov't
MeSH terms
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Adolescent
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Adult
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Aged
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Aged, 80 and over
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Antibody Specificity
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Antigens, CD / metabolism
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Autoantibodies / immunology*
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Cell Degranulation
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Child
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Child, Preschool
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Female
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G(M1) Ganglioside / immunology
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Gangliosides / immunology*
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Guillain-Barre Syndrome / blood
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Guillain-Barre Syndrome / immunology*
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Humans
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Immunoglobulin A / immunology*
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Immunoglobulin G / immunology*
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Leukocytes / immunology*
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Leukocytes / pathology
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Male
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Middle Aged
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Miller Fisher Syndrome / blood
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Miller Fisher Syndrome / immunology
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Receptors, Fc / metabolism
Substances
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Antigens, CD
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Autoantibodies
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Fc(alpha) receptor
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Gangliosides
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Immunoglobulin A
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Immunoglobulin G
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Receptors, Fc
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ganglioside, GD1b
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G(M1) Ganglioside
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GQ1b ganglioside