Successful liver transplantation across the ABO incompatibility barrier in 6 cases of biliary atresia

J Pediatr Surg. 2006 Dec;41(12):1976-9. doi: 10.1016/j.jpedsurg.2006.08.021.

Abstract

Background: The problem of ABO-incompatible liver transplantation still remains unsolved in older children. In this article, we report on our experience of 6 successful ABO-incompatible liver transplantations in patients with biliary atresia.

Material and methods: Six patients (ABO incompatibility type A-->O:1 case, B-->O:2 cases, A-->B:3 cases) were enrolled in this study; 3 patients were aged approximately 1 year and the other 3 ranged in age from 9 to 24 years at the time of transplantation. Each patient received perioperative plasma exchange, until the anti-donor blood-type antibody titers became less than 1:16, and also systemic multidrug immunosuppressive therapy (cyclophosphamide, prednisolone, and tacrolimus). We applied the protocol of intraportal infusion therapy (local administration of prostaglandin E(1), steroid, and gabexate mesilate via a portal vein catheter), splenectomy, and rituximab administration for the older group.

Results: Both the patient and graft survival rates remain at 100%, with the follow-up period of the patients ranging from 12 and 123 months. Acute cellular rejection occurred in 2 cases, and both were steroid sensitive. There was no incidence of humoral rejection. Although all cases developed viral infection, all recovered uneventfully with the administration of antiviral agents.

Conclusion: ABO-incompatible liver transplantation can be performed with a low risk of humoral rejection or late biliary complications using this combined antirejection strategy, even in older children.

MeSH terms

  • ABO Blood-Group System / immunology*
  • Adolescent
  • Adult
  • Alprostadil / administration & dosage
  • Biliary Atresia / surgery*
  • Child
  • Clinical Protocols
  • Gabexate / administration & dosage
  • Glucocorticoids / administration & dosage
  • Graft Rejection / prevention & control
  • Graft Survival / drug effects
  • Hematologic Agents / administration & dosage
  • Humans
  • Immunosuppressive Agents / therapeutic use
  • Infant
  • Infusions, Intravenous
  • Liver Transplantation / immunology*
  • Plasma Exchange
  • Portal Vein
  • Splenectomy
  • Survival Analysis
  • Treatment Outcome

Substances

  • ABO Blood-Group System
  • Glucocorticoids
  • Hematologic Agents
  • Immunosuppressive Agents
  • Gabexate
  • Alprostadil