Abstract
Aims:
To compare the sensitivity and specificity of the recently commercially available FLI-1 monoclonal (FLI-1m) antibody with the currently used antibodies [CD99 and FLI-1 polyclonal (FLI-1p)] in the diagnosis of Ewing's sarcoma/primitive neuroectodermal tumour (EWS/PNET) and to determine the diagnostic value of the EWSR1 (22q12) dual-colour, break-apart rearrangement probe fluorescence in situ hybridization (FISH) technique.
Materials and methods:
Forty-three cases of well-documented EWS/PNET and 15 non-EWS/PNET cases were retrieved from the archival files. Immunohistochemistry (IHC) for FLI-1p, FLI-1m and FISH analysis was performed.
Results:
The most sensitive and specific test panel for the diagnosis of EWS/PNET is the combination of CD99 and FLI-1p. FISH had a very high specificity (100%) but only a moderate sensitivity (50%).
Conclusion:
The combination of CD99 and FLI-1p is the method of choice for the diagnosis of EWS/PNET. EWRS1 (22q12) dual-colour, break-apart rearrangement probe FISH should be used as a confirmatory test in addition to CD99 and FLI1-p due to its high specificity.
MeSH terms
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12E7 Antigen
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Actins
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Algorithms
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Antibodies, Monoclonal / immunology*
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Antibodies, Neoplasm / immunology
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Antigens, CD / immunology*
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Biomarkers, Tumor / analysis
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Biomarkers, Tumor / genetics
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Bone Neoplasms / diagnosis*
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Bone Neoplasms / genetics
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Bone Neoplasms / immunology
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Cell Adhesion Molecules / immunology*
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Chromosome Aberrations
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Female
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Humans
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In Situ Hybridization, Fluorescence / methods
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Male
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Microfilament Proteins / genetics*
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Microfilament Proteins / immunology*
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Neoplasm Proteins / immunology
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Neuroectodermal Tumors, Primitive / diagnosis*
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Neuroectodermal Tumors, Primitive / genetics
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Neuroectodermal Tumors, Primitive / immunology
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Predictive Value of Tests
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ROC Curve
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Receptors, Cytoplasmic and Nuclear / genetics*
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Receptors, Cytoplasmic and Nuclear / immunology*
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Sarcoma, Ewing / diagnosis*
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Sarcoma, Ewing / genetics
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Sarcoma, Ewing / immunology
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Trans-Activators
Substances
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12E7 Antigen
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Actins
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Antibodies, Monoclonal
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Antibodies, Neoplasm
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Antigens, CD
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Biomarkers, Tumor
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CD99 protein, human
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Cell Adhesion Molecules
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FLII protein, human
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Microfilament Proteins
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Neoplasm Proteins
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Receptors, Cytoplasmic and Nuclear
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Trans-Activators