Errors in translation cause selective neurodegeneration

ACS Chem Biol. 2006 Oct 24;1(9):562-6. doi: 10.1021/cb6004068.

Abstract

The 3D structure of a protein is determined by the unique sequence of amino acid residues comprising the polypeptide chain. Sequence changes can cause protein misfolding, a potentially toxic phenomenon implicated in various neurodegenerative disorders. In a recent paper, translational misincorporation is proposed to be a new biochemical mechanism for generating mutant proteins that misfold and kill neurons.

Publication types

  • Review

MeSH terms

  • Animals
  • Humans
  • Models, Biological
  • Models, Chemical
  • Neurodegenerative Diseases / genetics*
  • Neurodegenerative Diseases / pathology*
  • Neurons / metabolism
  • Phenotype
  • Protein Biosynthesis*
  • Protein Conformation
  • Protein Denaturation
  • Protein Folding