Primary cerebellopontine angle craniopharyngioma in a patient with gardner syndrome. Case report and review of the literature

J Neurosurg. 2006 Aug;105(2):330-3. doi: 10.3171/jns.2006.105.2.330.

Abstract

The authors report on the case of a craniopharyngioma arising in the cerebellopontine angle (CPA) in a patient with Gardner syndrome. Although familial adenomatous polyposis (FAP) is associated with intracranial neoplasms, the current case is only the third reported craniopharyngioma in a patient with Gardner syndrome. Two of these tumors, including that of the current case, originated in the CPA, an unusual location for craniopharyngiomas. The literature concerning FAP and its associations with intracranial neoplasia, as well as the pathogenesis of craniopharyngiomas in the posterior fossa, is discussed.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adult
  • Cerebellar Neoplasms / diagnosis
  • Cerebellar Neoplasms / genetics*
  • Cerebellar Neoplasms / pathology
  • Cerebellar Neoplasms / surgery*
  • Cerebellopontine Angle / pathology*
  • Cerebellopontine Angle / surgery*
  • Cerebellum / pathology
  • Cerebellum / surgery
  • Craniopharyngioma / diagnosis
  • Craniopharyngioma / genetics
  • Craniopharyngioma / pathology
  • Craniopharyngioma / surgery*
  • Diagnosis, Differential
  • Fibroma / diagnosis
  • Fibroma / genetics
  • Fibroma / pathology
  • Fibroma / surgery
  • Gardner Syndrome / diagnosis
  • Gardner Syndrome / genetics
  • Gardner Syndrome / pathology
  • Gardner Syndrome / surgery*
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Neoplasms, Multiple Primary / diagnosis
  • Neoplasms, Multiple Primary / genetics
  • Neoplasms, Multiple Primary / pathology
  • Neoplasms, Multiple Primary / surgery
  • Scalp / pathology
  • Scalp / surgery
  • Skin Neoplasms / diagnosis
  • Skin Neoplasms / genetics
  • Skin Neoplasms / pathology
  • Skin Neoplasms / surgery