Histiocytic tumor of Meckel's cave. An intracranial equivalent of juvenile xanthogranuloma of the skin

Am J Surg Pathol. 1992 Jan;16(1):76-83.

Abstract

We present the case of a 7-year-old boy who had a solitary mass within Meckel's cave that recurred 6 weeks after the initial resection. The histological, immunohistochemical, electron-microscopical, and molecular genetical features established the lesion's histiocytic nature. Our findings showed that it was closely related to juvenile xanthogranuloma, a benign lesion that usually occurs in the skin but has not yet been histologically confirmed in the brain. The present tumor is different from other intracranial histiocytic and xanthogranulomatous lesions.

Publication types

  • Case Reports

MeSH terms

  • Acid Phosphatase / analysis
  • Actins / analysis
  • Alkaline Phosphatase / analysis
  • Antigens, CD / analysis
  • Blotting, Southern
  • Cell Transformation, Neoplastic / pathology
  • Child
  • Cranial Nerve Neoplasms / chemistry
  • Cranial Nerve Neoplasms / pathology*
  • Cranial Nerve Neoplasms / ultrastructure
  • DNA, Neoplasm / analysis
  • DNA, Neoplasm / genetics
  • Gene Rearrangement, T-Lymphocyte / genetics
  • Humans
  • Immunohistochemistry
  • Male
  • Microscopy, Electron
  • Skin Diseases / pathology*
  • Trigeminal Ganglion*
  • Xanthogranuloma, Juvenile / pathology*
  • alpha 1-Antichymotrypsin / analysis
  • alpha 1-Antitrypsin / analysis

Substances

  • Actins
  • Antigens, CD
  • DNA, Neoplasm
  • alpha 1-Antichymotrypsin
  • alpha 1-Antitrypsin
  • Alkaline Phosphatase
  • Acid Phosphatase