De novo subtelomeric deletion additional to an inherited apparently balanced reciprocal translocation

Fetal Diagn Ther. 2007;22(4):306-12. doi: 10.1159/000100797. Epub 2007 Mar 15.

Abstract

Objective: We describe the analysis of an apparently balanced inherited reciprocal translocation in a fetus presenting with multiple congenital abnormalities, characterize the structural chromosome rearrangement, and report an unexpected additional imbalance to the inherited rearrangement.

Methods: DNA microarray was used to screen for genomic imbalance in subtelomeric and interstitial critical regions. High-resolution comparative genomic hybridization was used to screen for genomic imbalance at a genome-wide level. Fluorescence in situ hybridization using whole-chromosome painting and specific probes was used to characterize the inherited translocation, and the size of the de novoadditional deletion.

Results: An unexpected additional deletion was found in 7qter on derivative 10 of the inherited maternal reciprocal translocation t(7;10)(q11.23; p14).

Conclusions: We show the usefulness of genome-wide and specific molecular cytogenetic techniques to explore apparently balanced rearrangements.

MeSH terms

  • Abnormalities, Multiple / diagnosis*
  • Abnormalities, Multiple / genetics
  • Abnormalities, Multiple / pathology
  • Abortion, Induced
  • Adult
  • Allelic Imbalance
  • Brain / abnormalities*
  • Brain / pathology
  • Chromosome Painting
  • Cranial Fossa, Posterior / abnormalities*
  • Cranial Fossa, Posterior / pathology
  • Cytogenetic Analysis
  • Female
  • Gene Deletion*
  • Heart Defects, Congenital / diagnosis*
  • Heart Defects, Congenital / genetics
  • Heart Defects, Congenital / pathology
  • Humans
  • Karyotyping
  • Oligonucleotide Array Sequence Analysis
  • Pregnancy
  • Prenatal Diagnosis / methods*
  • Telomere*
  • Translocation, Genetic*
  • Ultrasonography, Prenatal