Toxic epidermal necrolysis: 15 years' experience in a Dutch burns centre

J Eur Acad Dermatol Venereol. 2007 Jul;21(6):781-8. doi: 10.1111/j.1468-3083.2006.02082.x.

Abstract

Background: Toxic epidermal necrolysis (TEN) is a severe and potentially fatal drug reaction characterized by an extensive skin rash with blisters and exfoliation, frequently accompanied by mucositis. The wounds caused by TEN are similar to second-degree burns and severe cases may involve large areas of skin loss.

Objectives: Analysis of our results in patients with TEN and evaluation of the variety of therapeutic interventions that has been studied and suggested in TEN.

Patients/methods: Retrospective analysis of 19 consecutive patients with TEN treated in our burns centre between 1989 and 2004.

Results: Immediate withdrawal of any potentially fatal drug, maximum supportive care, and a restricted and tailored antibiotic, medical and surgical treatment regimen confined mortality to 21%, whereas prognosis scores like APACHE II and SCORTEN predicted mortality of 22 and 30%, respectively. A positive contribution of selective digestive decontamination is suggested but has yet to be established.

Conclusions: Because of a potentially fatal outcome, fast referral of a patient suspected of TEN to a specialized centre (mostly a burns unit or specialized dermatology centre) for expert wound management and tailored comprehensive care is strongly advised and contributes to survival.

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Burn Units
  • Child
  • Humans
  • Middle Aged
  • Netherlands / epidemiology
  • Prognosis
  • Referral and Consultation
  • Retrospective Studies
  • Stevens-Johnson Syndrome / mortality
  • Stevens-Johnson Syndrome / therapy*
  • Treatment Outcome