Identification of pristanoyl-CoA oxidase and phytanic acid decarboxylation in peroxisomes and mitochondria from human liver: implications for Zellweger syndrome

J Inherit Metab Dis. 1991;14(3):349-52. doi: 10.1007/BF01811700.

Authors

R J Wanders¹, C W van Roermund, C Jakobs, H J ten Brink

Affiliation

¹ Department of Paediatrics, University Hospital Amsterdam, The Netherlands.

PMID: 1770789
DOI: 10.1007/BF01811700

No abstract available

MeSH terms

Centrifugation, Density Gradient
Decarboxylation
Humans
Microbodies / enzymology
Microbodies / metabolism*
Mitochondria, Liver / enzymology
Mitochondria, Liver / metabolism*
Oxidoreductases / analysis*
Phytanic Acid / metabolism*
Zellweger Syndrome / enzymology
Zellweger Syndrome / metabolism*

Substances

Phytanic Acid
Oxidoreductases
pristanoyl-CoA oxidase