Alternative methionine degradation via the transamination pathway: an option for therapy for homocystinuria due to cystathionine synthase deficiency

J Inherit Metab Dis. 1991;14(3):375-8. doi: 10.1007/BF01811707.

Authors

H J Blom¹, G H Boers, A Tangerman, W A Gahl, J M Trijbels

Affiliation

¹ Department of Paediatrics, University Hospital Nijmegen, The Netherlands.

PMID: 1770796
DOI: 10.1007/BF01811707

No abstract available

Publication types

Research Support, Non-U.S. Gov't

MeSH terms

Animals
Carbon-Oxygen Lyases*
Homocystinuria / metabolism
Homocystinuria / therapy*
In Vitro Techniques
Liver / metabolism
Lyases / deficiency*
Methionine / metabolism*
Rats

Substances

Methionine
O-succinylhomoserine (thiol)-lyase
Lyases
Carbon-Oxygen Lyases