Oropharyngeal teratomas are rare congenital malformations that arise from all three basic germinal layers and form a high risk situation for the neonate. Their incidence is only sporadic and they are not associated with a high recurrence risk, although some cases of associated chromosomal aberrations have been described. In this case report we present the clinical course and the histopathological findings of a prenatal diagnosed stillborn infant with an oropharyngeal teratoma of the left maxilla by a 33-year-old primigravida woman at 40 weeks 5 days' gestation. Moreover we emphasize on the relevance of the prenatal diagnosis and visualisation of such fetal tumors not only because of their great importance on the obstetrical management but also for their critical contribution to the optimal treatment of the affected newborn.