Tumor suppressor CYLD regulates JNK-induced cell death in Drosophila

Dev Cell. 2007 Sep;13(3):446-54. doi: 10.1016/j.devcel.2007.07.012.

Abstract

CYLD encodes a tumor suppressor that is mutated in familial cylindromatosis. Despite biochemical and cell culture studies, the physiological functions of CYLD in animal development and tumorigenesis remain poorly understood. To address these questions, we generated Drosophila CYLD (dCYLD) mutant and transgenic flies expressing wild-type and mutant dCYLD proteins. Here we show that dCYLD is essential for JNK-dependent oxidative stress resistance and normal lifespan. Furthermore, dCYLD regulates TNF-induced JNK activation and cell death through dTRAF2, which acts downstream of the TNF receptor Wengen and upstream of the JNKK kinase dTAK1. We show that dCYLD encodes a deubiquitinating enzyme that deubiquitinates dTRAF2 and prevents dTRAF2 from ubiquitin-mediated proteolytic degradation. These data provide a molecular mechanism for the tumor suppressor function of this evolutionary conserved molecule by indicating that dCYLD plays a critical role in modulating TNF-JNK-mediated cell death.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Animals, Genetically Modified
  • Apoptosis / physiology
  • Cell Death / physiology
  • Deubiquitinating Enzyme CYLD
  • Drosophila / genetics
  • Drosophila / metabolism*
  • Drosophila Proteins / genetics
  • Drosophila Proteins / metabolism
  • Drosophila Proteins / physiology*
  • Genes, Insect
  • Genes, Tumor Suppressor
  • JNK Mitogen-Activated Protein Kinases / genetics
  • JNK Mitogen-Activated Protein Kinases / metabolism
  • JNK Mitogen-Activated Protein Kinases / physiology*
  • Longevity
  • Mutation
  • Oxidative Stress
  • Plasmids
  • Precipitin Tests
  • Signal Transduction
  • TNF Receptor-Associated Factor 2 / metabolism
  • Tumor Suppressor Proteins / genetics
  • Tumor Suppressor Proteins / metabolism
  • Tumor Suppressor Proteins / physiology*

Substances

  • Drosophila Proteins
  • TNF Receptor-Associated Factor 2
  • Tumor Suppressor Proteins
  • JNK Mitogen-Activated Protein Kinases
  • CYLD protein, Drosophila
  • Deubiquitinating Enzyme CYLD