Inter-alpha-trypsin inhibitor attenuates complement activation and complement-induced lung injury

J Immunol. 2007 Sep 15;179(6):4187-92. doi: 10.4049/jimmunol.179.6.4187.

Abstract

Complement activation is a central component of inflammation and sepsis and can lead to significant tissue injury. Complement factors are serum proteins that work through a cascade of proteolytic reactions to amplify proinflammatory signals. Inter-alpha-trypsin inhibitor (IaI) is an abundant serum protease inhibitor that contains potential complement-binding domains, and has been shown to improve survival in animal sepsis models. We hypothesized that IaI can bind complement and inhibit complement activation, thus ameliorating complement-dependent inflammation. We evaluated this hypothesis with in vitro complement activation assays and in vivo in a murine model of complement-dependent lung injury. We found that IaI inhibited complement activation through the classical and alternative pathways, inhibited complement-dependent phagocytosis in vitro, and reduced complement-dependent lung injury in vivo. This novel function of IaI provides a mechanistic explanation for its observed salutary effects in sepsis and opens new possibilities for its use as a treatment agent in inflammatory diseases.

Publication types

  • Research Support, N.I.H., Intramural

MeSH terms

  • Alpha-Globulins / deficiency
  • Alpha-Globulins / genetics
  • Alpha-Globulins / metabolism
  • Alpha-Globulins / physiology*
  • Animals
  • Complement Activation / genetics
  • Complement Activation / immunology*
  • Complement Inactivator Proteins / deficiency
  • Complement Inactivator Proteins / genetics
  • Complement Inactivator Proteins / metabolism
  • Complement Inactivator Proteins / physiology*
  • Complement System Proteins / metabolism
  • Complement System Proteins / toxicity*
  • Female
  • Immune Complex Diseases / immunology
  • Immune Complex Diseases / metabolism
  • Immune Complex Diseases / pathology
  • Immune Complex Diseases / prevention & control
  • Lung / immunology*
  • Lung / metabolism
  • Lung / pathology*
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • Phagocytosis / immunology
  • Protein Binding / immunology
  • Protein Subunits / deficiency
  • Protein Subunits / genetics
  • Protein Subunits / metabolism
  • Protein Subunits / physiology

Substances

  • Alpha-Globulins
  • Complement Inactivator Proteins
  • Protein Subunits
  • inter-alpha-inhibitor
  • Complement System Proteins