Antithymocyte globulin and cyclosporine for treatment of 44 children with hepatitis associated aplastic anemia

Haematologica. 2007 Dec;92(12):1687-90. doi: 10.3324/haematol.11359.

Abstract

We analyzed the outcomes of 44 children with hepatitis associated aplastic anemia (HAA) who received immunosuppressive therapy (IST) with antithymocyte globulin (ATG) and cyclosporine (CsA). Fourteen (31.8%) patients achieved complete response and 17 (38.6%) achieved partial response, for an overall response rate of 70.4% after 6 months. Seven non-responders received bone marrow transplantation from an HLA-matched unrelated donor and 6 out of 7 are alive. The probability of overall survival at 10 years was 88.3+/-4.9%, which supports the role of IST with ATG and CsA as treatment of choice for children with HAA without an HLA identical sibling donor.

Publication types

  • Multicenter Study
  • Randomized Controlled Trial

MeSH terms

  • Adolescent
  • Anemia, Aplastic / mortality
  • Anemia, Aplastic / therapy*
  • Antilymphocyte Serum / administration & dosage*
  • Bone Marrow Transplantation*
  • Child
  • Child, Preschool
  • Cyclosporine / administration & dosage*
  • Disease-Free Survival
  • Female
  • Follow-Up Studies
  • Hepatitis / pathology
  • Hepatitis / therapy*
  • Histocompatibility Testing
  • Humans
  • Immunosuppressive Agents / administration & dosage*
  • Infant
  • Male
  • Survival Rate
  • Transplantation, Homologous

Substances

  • Antilymphocyte Serum
  • Immunosuppressive Agents
  • Cyclosporine