A case of primary Epstein-Barr virus-associated cutaneous diffuse large B-cell lymphoma unassociated with iatrogenic or endogenous immune dysregulation

J Cutan Pathol. 2008 Jul;35(7):666-71. doi: 10.1111/j.1600-0560.2007.00859.x. Epub 2008 Jan 14.

Abstract

Cutaneous Epstein-Barr virus (EBV)-associated B-cell lymphoma (EBVBL) in non-immunocompromised patients is very rare. Here, we report a case of cutaneous EBVBL in a 72-year-old Japanese woman without any signs of immunosuppression. She showed repeated high fever and skin eruptions on the face, limbs and palms. Histological diagnosis was diffuse large B-cell lymphoma. EBV infection was detected by in situ hybridization and Southern blotting. Immunostaining for viral proteins showed the patient to be positive for latent membrane protein 1 (LMP-1) and negative for Epstein-Barr virus nuclear antigen-1 (EBNA-2), indicating that a type II latency EBV infection pattern.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Aged, 80 and over
  • Antigens, CD / analysis
  • DNA, Viral / analysis
  • Epstein-Barr Virus Infections / complications
  • Epstein-Barr Virus Infections / immunology*
  • Fatal Outcome
  • Female
  • Herpesvirus 4, Human / genetics
  • Herpesvirus 4, Human / isolation & purification*
  • Humans
  • Immunocompetence
  • Immunologic Techniques
  • Lymphoma, Large B-Cell, Diffuse / immunology
  • Lymphoma, Large B-Cell, Diffuse / pathology
  • Lymphoma, Large B-Cell, Diffuse / virology*
  • Male
  • Middle Aged
  • RNA, Viral / analysis
  • Skin Neoplasms / immunology
  • Skin Neoplasms / pathology
  • Skin Neoplasms / virology*
  • Viral Matrix Proteins / analysis
  • Virus Latency

Substances

  • Antigens, CD
  • DNA, Viral
  • EBV-associated membrane antigen, Epstein-Barr virus
  • RNA, Viral
  • Viral Matrix Proteins