Successful treatment of primary chronic osteomyelitis in SAPHO syndrome with bisphosphonates

J Dtsch Dermatol Ges. 2008 Aug;6(8):657-60. doi: 10.1111/j.1610-0387.2008.06588.x. Epub 2008 Feb 6.
[Article in English, German]

Abstract

The treatment of the painful osteomyelitis in patients with SAPHO syndrome (Synovitis, Acne, Pustulosis, Hyperostosis, Osteitis) is often a problem. A 53-year-old woman had experienced palmo-plantar pustular skin lesions for four years, and in the past two years complained about progressive breath-and movement-dependent pain of the sternum. On examination she had extensive palmoplantar pustules and a painful swelling in the area of the right sternoclavicular joint. The three-phase bone scintigraphy showed a strong focal enrichment in the right sternoclavicular joint and at the transition from the manubrium to the corpus sterni suggesting active osteo-chondritis. Initially prednisolone and ibuprofen were administered, but only the skin changes regressed. The strong sternal pain decreased only after infusion of 4 mg zoledronic acid over three days. In a follow-up examination after five months the patient was still free of pain. The bisphosphonates inhibit osteoclastic activity and lead to long-lasting improvement of osteo-articular complaints in the SAPHO syndrome.

Publication types

  • Case Reports

MeSH terms

  • Acquired Hyperostosis Syndrome / diagnosis*
  • Acquired Hyperostosis Syndrome / drug therapy*
  • Bone Density Conservation Agents / administration & dosage
  • Chronic Disease
  • Diphosphonates / administration & dosage*
  • Female
  • Humans
  • Middle Aged
  • Osteomyelitis / diagnosis*
  • Osteomyelitis / drug therapy*
  • Treatment Outcome

Substances

  • Bone Density Conservation Agents
  • Diphosphonates