Properdin deficiency in murine models of nonseptic shock

J Immunol. 2008 May 15;180(10):6962-9. doi: 10.4049/jimmunol.180.10.6962.

Abstract

Hereditary properdin deficiency is linked to susceptibility to meningococcal disease (Neisseria meningitidis serotypes Y and W-135) with high mortality. Its relative contribution toward the outcome of nonseptic shock has not been investigated. Using properdin-deficient C57BL/6 mice and their littermates, this study examines their survival of zymosan-induced and LPS-induced shock. Properdin-deficient mice were more resistant to zymosan shock compared with wild-type mice, which showed greater impairment of end-organ function 24 h after zymosan injection, higher TNF-alpha production by alveolar and peritoneal macrophages, higher TNF-alpha, and, inversely, lower IL-10 levels in peritoneal lavage and circulation and higher plasma C5a levels. Properdin-deficient mice showed significantly higher mortality in LPS shock, elevated TNF-alpha, and, inversely, reduced IL-10 production by peritoneal macrophages as well as lower plasma C5a levels compared with wild-type littermates. NO production by peritoneal macrophages and plasma alpha1-antitrypsin levels at 24 h after the injection of LPS or zymosan were decreased in properdin-deficient mice in both models, and fewer histopathologic changes in liver were observed in properdin-deficient animals. This study provides evidence that properdin deficiency attenuates zymosan-induced shock and exacerbates LPS-induced shock.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Complement C5a / metabolism
  • Disease Models, Animal
  • Enzyme-Linked Immunosorbent Assay
  • Fluorescent Antibody Technique
  • Interleukin-10 / metabolism
  • Lipopolysaccharides / toxicity*
  • Macrophage Activation / immunology
  • Macrophages / immunology
  • Macrophages / metabolism
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Mice, Mutant Strains
  • Nitric Oxide / biosynthesis
  • Properdin / deficiency*
  • Shock / chemically induced
  • Shock / metabolism*
  • Shock / physiopathology*
  • Tumor Necrosis Factor-alpha / metabolism
  • Zymosan / toxicity*
  • alpha 1-Antitrypsin / blood

Substances

  • Lipopolysaccharides
  • Tumor Necrosis Factor-alpha
  • alpha 1-Antitrypsin
  • Properdin
  • Interleukin-10
  • Nitric Oxide
  • Complement C5a
  • Zymosan