Hypohidrotic ectodermal dysplasia: a case report

Quintessence Int. 2008 Jan;39(1):81-6.

Abstract

Ectodermal dysplasias represent a large and complex group of diseases comprising more than 170 clinical conditions. They are caused by impaired development of the ectodermal appendages and characterized by a primary defect in at least one of the following tissues: nails, hair, sweat glands, or teeth. Ectodermal dysplasia has emotional consequences for affected individuals at early ages. This case report outlines a possible routine approach to restoring function and esthetics and aiding in the social interaction for a 9-year-old girl diagnosed with hypohidrotic ectodermal dysplasia at about 7 years of age.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Crowns
  • Dental Caries / therapy
  • Dental Prosthesis Design
  • Ectodermal Dysplasia / complications*
  • Female
  • Humans
  • Malocclusion / therapy
  • Mouth Rehabilitation*
  • Patient Care Planning
  • Periodontal Diseases / therapy
  • Tooth Abnormalities / therapy