Incidence of hepatotropic viruses in biliary atresia

Eur J Pediatr. 2009 Apr;168(4):469-76. doi: 10.1007/s00431-008-0774-2. Epub 2008 Jun 17.

Abstract

Biliary atresia (BA) is the most frequent indication for paediatric liver transplantation. We tested the hypothesis of a viral aetiology of this disease by screening liver samples of a large number of BA patients for the common human hepatotropic viruses. Moreover, we correlated our findings to the expression of Mx protein, which has been shown to be significantly up-regulated during viral infections. Seventy-four liver biopsies (taken during Kasai portoenterostomy) were tested by polymerase chain reaction (PCR) for DNA viruses (herpes simplex virus [HSV], Epstein-Barr virus [EBV], varicella zoster virus [VZV], cytomegalovirus [CMV], adenovirus, parvovirus B19 and polyoma BK) and RNA viruses (enteroviruses, rotavirus and reovirus 3). Mx protein expression was assessed by immunohistochemistry. Virus DNA/RNA was found in less than half of the biopsies (8/74 CMV, 1/74 adenovirus; 21/64 reovirus, 1/64 enterovirus). A limited number presented with double infection. Patients that had detectable viral RNA/DNA in their liver biopsies were significantly older than virus-free patients (P = 0.037). The majority (54/59) of the liver biopsies showed expression of Mx proteins in hepatocytes, bile ducts and epithelium. Our data suggest that the known hepatotropic viruses do not play a major role in the aetiology and progression of BA. Their incidence appears to be, rather, a secondary phenomenon. Nonetheless, the inflammatory response in the livers of BA patients mimics that observed during viral infections.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adenoviridae / isolation & purification
  • Biliary Atresia / epidemiology
  • Biliary Atresia / virology*
  • Biomarkers / metabolism
  • Comorbidity
  • Cytomegalovirus / isolation & purification
  • DNA, Viral / isolation & purification
  • Enterovirus / isolation & purification
  • Female
  • GTP-Binding Proteins / metabolism
  • Hepatitis Viruses / isolation & purification*
  • Hepatitis Viruses / metabolism
  • Hepatitis, Viral, Human / epidemiology*
  • Hepatitis, Viral, Human / metabolism
  • Hepatitis, Viral, Human / virology*
  • Herpesvirus 3, Human / isolation & purification
  • Herpesvirus 4, Human / isolation & purification
  • Humans
  • Incidence
  • Infant
  • Infant, Newborn
  • Liver / pathology
  • Liver / virology
  • Male
  • Mammalian orthoreovirus 3 / isolation & purification
  • Myxovirus Resistance Proteins
  • Parvovirus B19, Human / isolation & purification
  • Polyomavirus / isolation & purification
  • RNA, Viral / isolation & purification
  • Retrospective Studies
  • Rotavirus / isolation & purification
  • Simplexvirus / isolation & purification

Substances

  • Biomarkers
  • DNA, Viral
  • Myxovirus Resistance Proteins
  • RNA, Viral
  • GTP-Binding Proteins