Clinical variability in acro-cardio-facial-syndrome

Am J Med Genet A. 2008 Aug 1;146A(15):1977-9. doi: 10.1002/ajmg.a.32052.

Abstract

We report on a 25-year-old man with ectrodactyly and genital anomalies whose parents are first cousins. Their second child died 4 days after birth with severe limb defects and imperforate anus. Our patient may represent clinical variability of the acro-cardio-facial syndrome.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple / genetics*
  • Adult
  • Anus, Imperforate / genetics
  • Chromosome Banding
  • Consanguinity
  • Ectromelia / genetics
  • Female
  • Genitalia, Male / abnormalities*
  • Hand Deformities, Congenital / genetics*
  • Humans
  • Hypospadias / genetics*
  • Infant, Newborn
  • Male
  • Syndrome