Purpose: To report a partial steroid response of xanthoma disseminatum in a black African woman.
Design: Case report and literature review.
Methods: Histopathologic study of cutaneous tumour and clinical follow-up.
Results: A 32-year-old black African woman with mucocutaneous xanthomatosis and dysphonia, which partially responded to treatment with steroids.
Conclusions: Xanthoma dissseminatum is a rare condition for which there is no medical treatment. We reported the condition in a black African woman whose skin and CNS symptoms regressed remarkably within 22 weeks of steroid therapy.