Progressive spastic paraplegia: the combination of Scheuermann's disease, a short-segmented kyphosis and dysplastic thoracic spinous processes

Spinal Cord. 2009 Jul;47(7):570-2. doi: 10.1038/sc.2008.133. Epub 2008 Nov 11.

Abstract

Study design: Case report.

Objective: To describe a rare case of paraplegia in a patient with Scheuermann's disease and dysplastic thoracic spinous processes.

Setting: Spinal Cord Injury Center, Orthopaedic University Hospital Heidelberg, Heidelberg, Germany.

Clinical presentation: The authors report on a 15-year-old boy with progressive incomplete spastic paraplegia presenting segmental dysplastic thoracic spinous processes and Scheuermann's disease. The magnetic resonance imaging showed a kyphotic angulation at T 5/6 and signs of myelopathy. Hypoplastic thoracic processes and hypoplastic paraspinal muscles in the upper thoracic spine were observed intraoperatively. In this case, dorsoventral stabilization from T 4-7 was performed and the neurological outcome improved at follow-up (6 months).

Conclusion: Paraplegia can be accelerated in patients with Scheuermann's disease, severe kyphotic angulation and dysplastic posterior elements. After operative treatment, neurological recovery and a normal walking pattern were shown.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Disease Progression
  • Humans
  • Kyphosis / complications*
  • Kyphosis / diagnosis
  • Kyphosis / radiotherapy
  • Kyphosis / surgery
  • Magnetic Resonance Imaging / methods
  • Male
  • Paraplegia / complications*
  • Paraplegia / diagnosis
  • Paraplegia / surgery
  • Radiography
  • Scheuermann Disease / complications*
  • Scheuermann Disease / diagnosis
  • Scheuermann Disease / surgery
  • Thoracic Vertebrae / diagnostic imaging
  • Thoracic Vertebrae / pathology*
  • Thoracic Vertebrae / surgery