[Diagnostic significance of immunophenotyping and detection of gene rearrangement in subcutaneous panniculitis-like T-cell lymphoma]

Zhonghua Bing Li Xue Za Zhi. 2008 Jun;37(6):390-4.
[Article in Chinese]

Abstract

Objective: To explore the diagnostic implication of immunophenotyping and gene rearrangement in subcutaneous panniculitis-like T-cell lymphoma (SPTL).

Methods: According to the selection criteria of 2005 WHO-EORTC classification for cutaneous lymphomas, 20 SPTL patients were enrolled in this study. A 10-antibody panel was used for immunophenotyping and in addition, polymerase chain reaction for TCR gamma and IgH gene rearrangement and in situ hybridization for EBER1/2 were also employed.

Results: There were 9 males and 11 female with a mean age of 29.5 years. Immunophenotypic study showed that all the patients expressed one to three T-cell associated antigens (CD2, CD3 or CD45RO), 18 patients were positive for beta F1, 18 for CD8, 20 for TIA-1 and 16 for granzyme B. None of the patients expressed CD4, CD20 and CD56. TCR gamma gene rearrangement was found in 16 of 20 cases (80.0%) and none for IgH gene rearrangement. The positive rate of EBER1/2 was 25.0% (5/20).

Conclusions: Since the majority of SPTL patients show clonal TCR gene rearrangements, correlations among clinical presentation, histological features, immunophenotype and gene rearrangement data are considered important in confirming a diagnosis of SPTL.

MeSH terms

  • Adolescent
  • Adult
  • Antigens, CD20 / immunology
  • CD56 Antigen / analysis*
  • CD56 Antigen / immunology
  • Child
  • Female
  • Gene Rearrangement / genetics*
  • Humans
  • Immunophenotyping / methods*
  • In Situ Hybridization
  • Lymphoma, T-Cell / classification*
  • Lymphoma, T-Cell / diagnosis
  • Lymphoma, T-Cell / genetics
  • Lymphoma, T-Cell / immunology
  • Lymphoma, T-Cell, Cutaneous / classification
  • Lymphoma, T-Cell, Cutaneous / diagnosis*
  • Lymphoma, T-Cell, Cutaneous / genetics
  • Lymphoma, T-Cell, Cutaneous / immunology
  • Male
  • Middle Aged
  • Panniculitis
  • RNA, Viral / immunology
  • RNA, Viral / isolation & purification
  • Skin Neoplasms / immunology
  • Subcutaneous Tissue
  • Young Adult

Substances

  • Antigens, CD20
  • CD56 Antigen
  • Epstein-Barr virus encoded RNA 1
  • RNA, Viral