[Mutation screening of the dystrophin gene in 14 Chinese Duchenne/Becker muscular dystrophy patients without gross deletions]

Zhonghua Yi Xue Yi Chuan Xue Za Zhi. 2008 Dec;25(6):633-6.
[Article in Chinese]

Abstract

Objective: To search for the dystrophin gene mutations of Duchenne muscular dystrophy (DMD) patients without gross deletions, in order to offer accurate genetic counseling and prenatal diagnosis for those families.

Methods: All 79 exons of the dystrophin gene as well as its 5'-UTR and 3'-UTR of 14 Chinese DMD/Becker muscular dystrphy (BMD) patients without detectable gross deletions were screened by denaturing high performance liquid chromatography (DHPLC) and heteroduplex fragments were identified by subsequent sequencing.

Results: Seven causative point mutations, including two novel ones, were detected in 7 patients. Fourteen known polymorphisms and 7 unknown intronic variations were also detected. Five mothers of the patients were obligate carriers.

Conclusion: DHPLC is an efficient way of identifying point mutations and the female carriers in DMD families.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Asian People / genetics*
  • Base Sequence
  • Child
  • Child, Preschool
  • DNA Mutational Analysis
  • Dystrophin / genetics*
  • Exons / genetics
  • Female
  • Genetic Counseling
  • Genetic Testing / methods*
  • Humans
  • Introns / genetics
  • Male
  • Muscular Dystrophy, Duchenne / diagnosis*
  • Muscular Dystrophy, Duchenne / genetics*
  • Point Mutation
  • Polymorphism, Genetic
  • Pregnancy
  • Prenatal Diagnosis
  • Sequence Deletion / genetics*

Substances

  • Dystrophin